BILL ANALYSIS                                                                                                                                                                                                    



                                                                  AB 1307
                                                                  Page  1


          ASSEMBLY THIRD READING
          AB 1307 (Buchanan)
          As Amended May 5, 2009
          Majority vote 

           HEALTH              15-1        APPROPRIATIONS      11-1        
           
           ------------------------------------------------------------------- 
          |Ayes:|Jones, Fletcher, Adams,   |Ayes:|De Leon, Ammiano, Charles   |
          |     |Block, Carter, Conway, De |     |Calderon, Davis, Fuentes,   |
          |     |La Torre,                 |     |Hall, John A. Perez, Price, |
          |     |De Leon, Emmerson,        |     |Skinner, Solorio, Torlakson |
          |     |Hayashi, Hernandez,       |     |                            |
          |     |Bonnie Lowenthal, Nava,   |     |                            |
          |     |V. Manuel Perez, Salas    |     |                            |
          |     |                          |     |                            |
          |-----+--------------------------+-----+----------------------------|
          |Nays:|Gaines                    |Nays:|Nielsen                     |
          |     |                          |     |                            |
           ------------------------------------------------------------------- 
           SUMMARY  :  Requires the Department of Public Health (DPH) to  
          consider including in the Newborn Screening Program (NSP)  
          screening for all conditions recommended by the American College  
          of Medical Genetics (ACMG), as specified.  Specifically,  this  
          bill  requires DPH to:  

          1)Consider including in the NSP screening for all conditions  
            that ACMG defines in its most recent recommendations as "core  
            panel" or "secondary targets," or by another advisory body  
            appointed by the Secretary of the United States (U.S.)  
            Department of Health and Human Services (DHHS) to make  
            recommendations for newborn screening. 

          2)Implement screening according to recommendations within one  
            year of receipt of the recommendations of ACMG or other  
            DHHS-approved entity, unless DPH determines the screening is  
            not necessary for advancing newborn health, and notifies the  
            appropriate committees of jurisdiction in the Legislature of  
            this determination. 
           
          EXISTING LAW  :

          1)Requires DPH screening of newborns to include numerous  
            specified disorders, and to provide information about these  








                                                                  AB 1307
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            disorders and available testing resources to all women  
            receiving prenatal care and all women admitted to a hospital  
            for a delivery. 

          2)In regulations, requires each newborn to be tested for  
            specified genetic disorders, except if the parents object  
            based on personal beliefs. 

          3)Establishes the Genetic Disease Testing Fund (Fund) in the  
            State Treasury, states the intent of the Legislature that the  
            Fund be fully fee-supported, and authorizes DPH to collect  
            fees for screening tests. 

           FISCAL EFFECT  :  According to the Assembly Appropriations  
          Committee analysis, this bill has no direct fiscal impact. 

           COMMENTS  :   The author of this bill states that screening  
          newborns to detect genetic disorders such as sickle-cell anemia  
          and phenylketonuria can prevent severe disability, mental  
          retardation, or even death.  The author states the development  
          of better screening tools prompted the federal Maternal and  
          Child Health Bureau of the Health Resources and Services  
          Administration (HRSA) to commission ACMG to prepare a report on  
          newborn screening and recommend a uniform panel of conditions  
          for which newborns should be screened.  According to the author,  
          this bill is needed because greater uniformity among newborn  
          screening programs would benefit families, professionals, and  
          public health agencies.  The author contends that newborn  
          screening may also save the state money on future medical costs  
          based on early detection and access to treatment of disorders. 

          Newborn screening in the U.S. is a state-based public health  
          program that began over 40 years ago.  States and territories  
          require screening of all infants born in their jurisdiction for  
          disorders that may not otherwise be detected before  
          developmental disability or death occurs (babies with these  
          disorders typically appear normal at birth).  According to DPH,  
          effective treatments are available for most, but not all,  
          diseases detected by NSP, and treatments may include special  
          diets or medications.  ACMG examined costs and benefits of  
          newborn screening and concluded that most newborn screening  
          programs improve outcomes and reduce costs.  

          In 2006, the journal Genetics in Medicine published the ACMG  








                                                                  AB 1307
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          guidelines for a uniform newborn screening panel and system,  
          which HRSA had requested.  To develop these recommendations,  
          ACMG convened a group of newborn screening experts who evaluated  
          genetic conditions based on explicit criteria, surveyed hundreds  
          of experts from the U.S. and other countries, and applied  
          specified criteria to develop recommendations.  The ACMG  
          workgroup categorized conditions as:  1) "core panel" (29  
          conditions); 2) "secondary targets," which means these  
          conditions are part of the differential diagnosis for conditions  
          on the core panel, are clinically significant but lack effective  
          treatment, or may have other clinical significance (25  
          conditions); and, 3) not appropriate for newborn screening. 

          According to DPH, California currently tests for 76 genetic  
          disorders, including  all  of the 29 disorders defined by ACMG as  
          core panel, and all except one of the conditions ACMG defines as  
          secondary targets.  The secondary target for which NSP no longer  
          screens is galactokinase deficiency, which DPH states was  
          extremely rare and required a separate test.  DPH states that  
          each year in California, approximately one in every 760 babies,  
          or a total of approximately 750 babies, are born with a genetic  
          disease detected by NSP.  

          DPH states disorders are evaluated for inclusion in the  
          screening program based on the following criteria:  1) important  
          health problem in terms of frequency, seriousness, and high  
          costs of care; 2) associated with disease/known symptoms; 3)  
          availability of effective treatment that improves quality of  
          life; 4) can be detected reliably and economically; and, 5)  
          existence of adequate methods of confirmation and follow-up.   
          DPH also states other considerations, including the number of  
          babies screened daily, may affect the decision to add disorders  
          to NSP.  DPH states NSP will add one disorder, severe combined  
          immune deficiency, when the ACMG finalizes its recommendation.   
          NSP is also reviewing five lysosomal storage disorders for  
          consideration, and will consider implementing these tests when  
          ACMG and the March of Dimes officially recommend them.


           Analysis Prepared by  :  Allegra Kim / HEALTH / (916) 319-2097 


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