BILL ANALYSIS                                                                                                                                                                                                    



                                                                  SJR 23
                                                                  Page  1

          Date of Hearing:   June 22, 2010

                            ASSEMBLY COMMITTEE ON HEALTH
                              William W. Monning, Chair
                    SJR 23 (Simitian) - As Amended:  June 15, 2010

           SENATE VOTE  :   32-0
           
          SUBJECT  :   Mitochondrial disease: federal support for research.

           SUMMARY  :   Urges the President and Congress to support research  
          for mitochondrial disease and makes various findings and  
          declarations relating to mitochondrial disease.

           EXISTING LAW  :

          1)Establishes the National Institutes of Health (NIH) within the  
            United States Department of Health and Human Services to  
            conduct and support medical research.

          2)Establishes the state Department of Public Health to, among  
            other things, research various public health problems, collect  
            and manage relevant health data, and award grants.

           FISCAL EFFECT  :   None

           COMMENTS  : 

           1)PURPOSE OF THIS RESOLUTION  .  According to the author, this  
            resolution is intended to urge the President and Congress to  
            significantly expand support for mitochondrial research and  
            improve public understanding of mitochondrial dysfunction by  
            complementing efforts at the federal level to draw attention  
            to mitochondrial disease research and treatment.

           2)BACKGROUND  .  Mitochondria are specialized compartments present  
            in every cell of the body, except red blood cells, that are  
            responsible for creating most of the energy needed by the body  
            to sustain life and support growth.  According to information  
            from the United Mitochondrial Disease Foundation,  
            mitochondrial disease results from failures of the  
            mitochondria to generate energy within the cell.  If this  
            process is repeated throughout the body, whole systems begin  
            to fail, and the life of the person in whom this is happening  
            is severely compromised.  Diseases of the mitochondria cause  








                                                                  SJR 23
                                                                  Page  2

            the most damage to cells of the brain, heart, liver, skeletal  
            muscles, kidney and the endocrine and respiratory systems.
          Depending on which cells are affected, symptoms may include loss  
            of motor control, muscle weakness and pain, gastro-intestinal  
            disorders and swallowing difficulties, poor growth, cardiac  
            disease, liver disease, diabetes, respiratory complications,  
            seizures, visual or hearing problems, developmental delays,  
            and susceptibility to infection.  The National Institute of  
            Environmental Health Sciences reports that half of those  
            affected by mitochondrial disease are children who show  
            symptoms before age five and approximately 80% of these  
            children will not survive beyond the age of 20.  There is no  
            treatment or cure for any of these rare diseases.

           3)NIH OFFICE OF RARE DISEASES RESEARCH  .  The Office of Rare  
            Diseases Research (ORDR) was established in 1993 within NIH to  
            coordinate and support research to respond to the needs of  
            patients who have any one of the more than 6,800 rare diseases  
            known today.  Among other things, the ORDR advises NIH on an  
            agenda for conducting rare diseases research and reports to  
            Congress and the public about NIH-supported scientific rare  
            diseases research advances and future plans; identifies and  
            responds to scientific opportunities and builds international  
            research collaborations; supports a program to develop new  
            genetic tests that are made available to the public;  
            cosponsors the Genetic and Rare Diseases Information Center;  
            and, provides opportunities for patient support groups to  
            become partners with the NIH, to better understand NIH  
            research programs, and to gain better access to NIH research  
            opportunities.  The NIH reports that many of its institutes  
            are currently supporting research relevant to mitochondrial  
            function and dysfunction; it has committed to establishing a  
            mitochondrial research initiative that would involve all NIH  
            institutes, and has awarded grant funding for mitochondrial  
            research.   

           4)RECENT FEDERAL ACTION  .  Two measures introduced in Congress in  
            2009, H.R. 3502 (McDermott) and S. 2858 (Boxer) seek to  
            establish a separate Office of Mitochondrial Medicine (Office)  
            at NIH.  The Office would be tasked with developing a plan to  
            improve coordination of research related to mitochondrial  
            medicine among the national research institutes and between  
            the NIH and outside researchers.  It would also be responsible  
            for providing training to scientists, health professionals,  
            and health care providers on research and diagnosis of  








                                                                  SJR 23
                                                                  Page  3

            mitochondrial disease and dysfunction.  Additionally, the  
            Office would be required to annually award grants for these  
            purposes and establish Mitochondrial Medicine Centers of  
            Excellence.  Lastly, the Office would be responsible for  
            creating a national registry to maintain and share medical  
            information collected from patients with mitochondrial disease  
            and dysfunction, and a national biorepository to collect  
            tissues and DNA from these patients for the purpose of  
            furthering research efforts.  

           5)PRIOR LEGISLATION  .  ACR 25 (Miller), Resolution Chapter 15,  
            Statutes of 2009, proclaims the third week of September as  
            Mitochondrial Disease Awareness Week.

           6)SUPPORT  .  The Association of Regional Center Agencies writes  
            that it fully supports additional federal funds to conduct  
            more extensive research into the causes of mitochondrial  
            diseases and dysfunctions associated with such disorders as  
            Parkinson's, Alzheimer's and autism because additional  
            research could help stem the rise of these disorders.

           REGISTERED SUPPORT / OPPOSITION  :

           Support 
           
          Association of Regional Center Agencies
          Numerous individuals
           
            Opposition 
           
          None on file.


           Analysis Prepared by  :    Cassie Rafanan / HEALTH / (916)  
          319-2097