BILL ANALYSIS                                                                                                                                                                                                    



                                                                  SJR 23
                                                                  Page  1


          SENATE THIRD READING
          SJR 23 (Simitian)
          As Amended June 15, 2010
          Majority vote 

           SENATE VOTE  :32-0  
           
           HEALTH              19-0                                        
           
           -------------------------------- 
          |Ayes:|Monning, Fletcher,        |
          |     |Ammiano, Carter, Conway,  |
          |     |De La Torre, De Leon,     |
          |     |Eng, Gaines, Hayashi,     |
          |     |Hernandez, Jones, Bonnie  |
          |     |Lowenthal, Nava,          |
          |     |V. Manuel Perez, Salas,   |
          |     |Smyth, Audra Strickland,  |
          |     |Gilmore                   |
          |     |                          |
           -------------------------------- 
           SUMMARY  :  Urges the President and Congress to support research  
          for mitochondrial disease and makes various findings and  
          declarations relating to mitochondrial disease.

           EXISTING LAW  :

          1)Establishes the National Institutes of Health (NIH) within the  
            United States Department of Health and Human Services to  
            conduct and support medical research.

          2)Establishes the state Department of Public Health to, among  
            other things, research various public health problems, collect  
            and manage relevant health data, and award grants.

           FISCAL EFFECT  :  None

           COMMENTS  :  According to the author, this resolution is intended  
          to urge the President and Congress to significantly expand  
          support for mitochondrial research and improve public  
          understanding of mitochondrial dysfunction by complementing  
          efforts at the federal level to draw attention to mitochondrial  
          disease research and treatment.









                                                                  SJR 23
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          Mitochondria are specialized compartments present in every cell  
          of the body, except red blood cells, that are responsible for  
          creating most of the energy needed by the body to sustain life  
          and support growth.  According to information from the United  
          Mitochondrial Disease Foundation, mitochondrial disease results  
          from failures of the mitochondria to generate energy within the  
          cell.  If this process is repeated throughout the body, whole  
          systems begin to fail, and the life of the person in whom this  
          is happening is severely compromised.  Diseases of the  
          mitochondria cause the most damage to cells of the brain, heart,  
          liver, skeletal muscles, kidney and the endocrine and  
          respiratory systems.  Depending on which cells are affected,  
          symptoms may include loss of motor control, muscle weakness and  
          pain, gastro-intestinal disorders and swallowing difficulties,  
          poor growth, cardiac disease, liver disease, diabetes,  
          respiratory complications, seizures, visual or hearing problems,  
          developmental delays, and susceptibility to infection.  The  
          National Institute of Environmental Health Sciences reports that  
          half of those affected by mitochondrial disease are children who  
          show symptoms before age five and approximately 80% of these  
          children will not survive beyond the age of 20.  There is no  
          treatment or cure for any of these rare diseases.
          The Office of Rare Diseases Research was established in 1993  
          within NIH to coordinate and support research to respond to the  
          needs of patients who have any one of the more than 6,800 rare  
          diseases known today.  Among other things, the ORDR advises NIH  
          on an agenda for conducting rare diseases research and reports  
          to Congress and the public about NIH-supported scientific rare  
          diseases research advances and future plans; identifies and  
          responds to scientific opportunities and builds international  
          research collaborations; supports a program to develop new  
          genetic tests that are made available to the public; cosponsors  
          the Genetic and Rare Diseases Information Center; and, provides  
          opportunities for patient support groups to become partners with  
          the NIH, to better understand NIH research programs, and to gain  
          better access to NIH research opportunities.  The NIH reports  
          that many of its institutes are currently supporting research  
          relevant to mitochondrial function and dysfunction; it has  
          committed to establishing a mitochondrial research initiative  
          that would involve all NIH institutes, and has awarded grant  
          funding for mitochondrial research.

          The Association of Regional Center Agencies writes in support  
          that additional federal funds to conduct more extensive research  








                                                                  SJR 23
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          into the causes of mitochondrial diseases and dysfunctions  
          associated with such disorders as Parkinson's, Alzheimer's and  
          autism are needed because the additional research could help  
          stem the rise of these disorders.


           Analysis Prepared by  :    Cassie Rafanan / HEALTH / (916)  
          319-2097 


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